Table 3 Results of the Systemic Disease Activity score (ESSDAI) of pediatric SS patients (n = 54)

ESSDAI score (mean ± SD)

4.91 ± 2.71

4.53 ± 2.44

5.55 ± 3.07

0.184

ESSDAI domains (score ≥ 1)

 Constitutional (%)

29(53.7)

19(55.9)

10(50.0)

0.675

 Lymphadenopathy (%)

20(37.0)

13(38.2)

7(35.0)

0.812

 Glandular (%)

4(53.7)

2(5.9)

2(10.0)

0.622^*

 Articular (%)

16(29.6)

6(17.6)

10(50.0)

0.012

 Cutaneous (%)

25(46.3)

14(41.2)

11(55.0)

0.325

 Pulmonary (%)

1(1.9)

0(0.0)

1(5.0)

0.370^*

 Renal (%)

15(27.8)

9(26.5)

6(30.0)

0.780

 Muscular (%)

3(5.6)

3(8.8)

0(0.0)

0.287^*

 PNS (%)

2(3.7)

1(2.9)

1(5.0)

1.000^*

 CNS (%)

3(5.6)

1(2.9)

2(10.0)

0.548^*

 Haematological (%)

15(27.8)

10(29.4)

5(25.0)

0.727

 Biological (%)

41(75.9)

24(70.6)

17(85.0)

0.329^*