Table 4 Comparison of demographic data and family medical history of patients with extreme periodic fever, aphthous stomatitis, pharyngitis, and cervical adenitis (ePFAPA), between those who met these criteria after steroid treatment (erPFAPA) and those who met the criteria upon first presentation
Variables | erPFAPA | ePFAPA upon presentation | P value |
|---|---|---|---|
Male sex, n (%) | 15/25 (60%) | 16/22 (73%) | 0.36 |
Mediterranean ancestry, n (%) | 9/24 (38%) | 12/18 (67%) | 0.06 |
Sephardic, n (%) | 9/24 (38%) | 11/18 (61%) | 0.13 |
Arabic, n (%) | 0 (0%) | 1/18 (5.6%) | 0.43 |
Ashkenazi ancestry, n (%) | 0 (0%) | 1/18 (5.6%) | 0.43 |
Multiethnic ancestry, n (%) | 15/24 (62%) | 5/18 (28%) | 0.03 |
Consanguinity, n (%) | 0 (%) | 0 (0%) | |
Family history of presumed PFAPA*, n (%) | 8/24 (33%) | 6/20 (30%) | 0.81 |
Family history of FMF, n (%) | 9/24 (38%) | 5/19 (26%) | 0.44 |
Family history of tonsillectomy, n (%) | 2/16 (12%) | 3/12 (25%) | 0.62 |