Table 1 Comparison of demographic data and family medical history between patients with extreme periodic fever, aphthous stomatitis, pharyngitis, and cervical adenitis (ePFAPA) and non-extreme PFAPA (nPFAPA)
Variables | ePFAPA | nPFAPA | P value |
|---|---|---|---|
Male sex, n (%) | 31/47 (66%) | 173/318 (54%) | 0.14 |
Mediterranean ancestry, n (%) | 21/42 (50%) | 149/299 (50%) | 0.98 |
Sephardic, n (%) | 20/42 (48%) | 105/299 (35%) | 0.12 |
Arabic, n (%) | 1/42 (2%) | 44/299 (15%) | 0.027 |
Ashkenazi ancestry, n (%) | 1/42 (2%) | 12/299 (4%) | > 0.99 |
Multiethnic ancestry, n (%) | 20/42 (48%) | 138/299 (46%) | 0.86 |
Consanguinity, n (%) | 0 (0%) | 6/296 (2%) | > 0.99 |
Family history of presumed PFAPA*, n (%) | 15/44 (34%) | 95/298 (32%) | 0.76 |
Family history of FMF, n (%) | 14/43 (33%) | 66/304 (22%) | 0.11 |
Family history of tonsillectomy, n (%) | 5/28 (18%) | 25/203 (12%) | 0.39 |