From: Proceedings of the 28th European Paediatric Rheumatology Congress (PReS 2022)
 | ANA- at 2y | ANA+ at 2y |
---|---|---|
Patients (n) | 4 | 11 |
Female n(%) | 3 (25) | 10 (9) |
Age (mean (SD)) | 13.80 (1.91) | 13.45 (2.72) |
Disease duration (mean (SD)) | 6.47 (4.22) | 6.17 (2.71) |
SLICC criteria: | ||
 Acute cutaneous, n (%) | 4 (100.0) | 6 (54.5) |
 Chronic cutaneous, n (%) | 0 (0.0) | 0 (0.0) |
 Alopecia, n (%) | 0 (0.0) | 1 (9.1) |
 Oral or nasal ulcers, n (%) | 2 (50.0) | 7 (63.6) |
 Arthritis, n (%) | 3 (75.0) | 4 (36.4) |
 Serositis, n (%) | 0 (0.0) | 2 (18.2) |
 Renal, n (%) | 1 (25.0) | 2 (18.2) |
 Neurological, n (%) | 0 (0.0) | 0 (0.0) |
 Hemolytic anemia, n (%) | 1 (25.0) | 4 (36.4) |
 Leukopenia, n (%) | 4 (100.0) | 9 (81.8) |
 Thrombocytopenia, n (%) | 3 (75.0) | 5 (45.5) |
 ANA+, n (%) | 4 (100.0) | 11 (100.0) |
 Anti-dsDNA+, n (%) | 4 (100.0) | 11 (100.0) |
 Anti-Sm+, n (%) | 1 (25.0) | 2 (18.2) |
 LAC, n (%) | 0 (0.0) | 1 (9.1) |
 anti-cardiolipin, n (%) | 2 (50.0) | 2 (18.2) |
 anti-beta2GPI+, n (%) | 2 (50.0) | 2 (18.2) |
 Low complement, n (%) | 4 (100.0) | 11 (100.0) |
 C3, mean (SD) mg/dL | 40.25 (5.51) | 52.73 (20.81) |
 C4, mean (SD) mg/dL | 3.67 (2.89) | 4.60 (2.72) |
 SLEDAI at diagnosis, mean (SD) | 12.75 (4.50) | 12.18 (7.14) |
SLEDAI at last follow-up, mean (SD) | 0.00 (0.00) | 1.36 (1.43) |
Treatment: | ||
 PDN, n (%) | 3 (75.0) | 11 (100.0) |
 HCQ, n (%) | 4 (100.0) | 11 (100.0) |
 MMF, n (%) | 4 (100.0) | 11 (100.0) |
 RTX, n (%) | 0 (0.0) | 2 (18.2) |