Table 1 (abstract P281). See text for description
From: Proceedings of the 28th European Paediatric Rheumatology Congress (PReS 2022)
Time interval between onset of symptoms and presentation (months) | Total number (n) | Age at onset (years) | Calcinosis | ILD | Lipodystrophy | GI vasculitis | Respiratory muscle weakness | Mortality |
0-3 | 38 | 73.4 | 7 (18.4%) | 2 (5.2%) | 4 (10.5%) | 5 (13.1%) | 3 (7.8%) | 5 (13.1%) |
3-6 | 28 | 63.9 | 6 (21.4%) | 5 (14.2%) | 1 (3.5%) | 1 (3.5%) | 4 (14.2%) | 3 (10.7%) |
6-12 | 31 | 6.53.4 | 4 (12.9%) | 3 (9.6%) | 2 (6.4%) | 1 (3.2%) | 3 (9.6%) | 2 (6.4%) |
≥12 | 43 | 6.43.1 | 18 (41.8%) | 6 (11.6%) | 10 (23.2%) | 0 (0%) | 3 (6.9%) | 2 (4.6%) |