Table 1 (abstract P240). See text for description
From: Proceedings of the 28th European Paediatric Rheumatology Congress (PReS 2022)
Spirometry | Pre treatment | 1 Year of treatment |
|---|---|---|
FEV1 (L) | 0.92 (46%) | 1.49 (65%) |
FVC (L) | 0.98 (46%) | 1.50 (61%) |
FEV1/FVC (%) | 93.88 | 99.33 |
SpO2 in room air | 88% | 99% |
6minute walk test | Unable to perform | Distance- 486.7m |