Table 1 (abstract P214). Performance against audit standards
From: Proceedings of the 28th European Paediatric Rheumatology Congress (PReS 2022)
Audit Standard | JSLE | JDM | JSSc | MCTD |
|---|---|---|---|---|
Evaluated for respiratory symptoms and signs at diagnosis and every 6 months | 18/30 (60) | 13/32 (41) | 1/5 (20) | 4/11 (36) |
Patients with respiratory symptoms and signs should have CXR and PFT including DLCO | 4/10 (40) | 2/5 (40) | 0/1 (0) | 3/5 (60) |
Patients with concerns re ILD on initial investigation should have HRCT chest | 4/5 (80) | 1/3 (33) | 2/2 (100) | 2/3 (67) |
Evaluated for cardiac symptoms and signs at diagnosis and every 6 months | 20/30 (67) | 14/32 (44) | 2/5 (40) | 4/11 (36) |
Patients with cardiac symptoms and/or signs should have echo and ECG | 5/8 (63) | 2/4 (50) | - | 3/6 (50) |
JSLE: Patients should have a CXR at diagnosis | 24/33 (73) | - | - | - |
JSLE: Patients with exertional intolerance should have CXR, PFT (with DLCO), ECG and echo | 2/7 (29) | - | - | - |
JDM/JSSc: All patients should have PFT including CO diffusion at diagnosis (JSSc: Patients should have PFT including CO diffusion every 6 months) | - | 6/32 (19) | 5/6 (83) 0/5 (0) | - |
JSLE/JDM: All patients should have an ECG at diagnosis | 20/33 (61) | 16/32 (50) | - | - |
JSLE/JDM: Patients should have an echo at diagnosis | 23/33 (70) | 11/32 (34) | - | - |
JSSc: Patients should have an echo every 6 months | - | - | 0/5 (0) | - |