From: Proceedings of the 28th European Paediatric Rheumatology Congress (PReS 2022)
Mean Age at Onset | 9.8 years (2-16) |
Sex Ratio F : M | 2.6 :1 |
Average Diagnostic delay | 7 months |
Fever at Onset | 3 / 11 (27%) |
Bone Involvement | |
 Tibia | 9/11 (82%) |
 Clavicles | 4 / 11 (36%) |
 Metacarpals & Metatarsals | 2 / 11 (18%) |
 Spinal leions | 2/11 (18%) |
 Calcaneum , Ribs , Femur | 2/11 (18%) |
 Scapula , Navicular , Humerus , Ulna | 1 / 11 (9%) |
Which region of bone was involved | |
 Metaphysis | 7 / 11 (63%) |
 Epiphysis & Diaphysis | 4 / 11 (36%) |
Type of Lesion at Onset | |
 Mixed | 6 / 11 (54%) |
 Lytic or Sclerotic | 5 / 11 (46%) |
 Skin Lesions | 3 / 11 (27%) |
 Elevated CRP +/- ESR at Onset | 6 / 11 (54%) |
Imaging modality used for Diagnosis | |
 Bone Scan | 8 / 11 (72%) |
 MRI | 8 / 11 (72%) |
 CT Scan | 4 / 11 (36%) |
 PET Scan | 2 / 11 (18%) |
 Bone Biopsy | 6 / 11 ( 54% ) |
Medications used in our Patients | |
 NSAIDs | 11 / 11 (100%) |
 Bisphosphonates (BPs) | 5 / 11 (46%) |
 BPs used in Spinal Lesion | 2 / 11 (18%) |
 MTX | 3 / 11 ( 27%) |
 TNF Inhibitors | 2 / 11 (18%) |
 TNFi used in Spinal Lesion | 1 / 11 (9%) |
Follow Up Details | |
 Average number of flares | 3 |
 Status not known due to lost on follow up | 4 / 11 (36%) |
 Inactive disease as per last follow up | 5 / 11 (54%) |
 Flare as per last follow up | 2 / 11 (18%) |