Table 1 (abstract P407). See text for description
From: Proceedings of the 28th European Paediatric Rheumatology Congress (PReS 2022)
Patient | A | B | C | D | E | F | G | H | I |
Age of presentation | 7 | 9 | 15 | 11 | 12 | 14 | 12 | 13 | 11 |
Delay in months Median: 24 (IQR:10-36) | 24 | 108 | 6 | 36 | 2 | 36 | 24 | 18 | 10 |
Presenting complaints | MSK ILD | MSK Red Eye Cataract Caries | ITP MSK HTN NPS Caries | MSK NPS PNS | ITP | PP MSK | IAV PP | IAV MSK PP | PP |
Initial Diagnosis | p-JIA | U-CTD | SLE | p-JIA | U-CTD | RTA | IAV RTA | IAV AIPS RTA | FS |
Symptoms | |||||||||
 1. Oral dryness | 1 | 1 | 1 | 2 | 1 | 1 | - | 1 |  |
 2. Ocular dryness | 2 |  |  |  |  |  |  | 2 | 2 |
 3. Parotid swelling |  |  | 3 |  |  | 3 |  | 3 |  |
Objective evidence | |||||||||
 1. Schirmer’s test ≤5 mm (Y/N) | (N) | (Y) | (N) | (Y) | (N) | (N) | (N) | (Y) | (Y) |
 2. Minor Salivary gland foci ≥1 (Y/N) | (Y) | (N) | (N) | (N) | ND | ND | ND | ND | ND |
Additional Test positive | |||||||||
 1. RF Positive | 1 | 3 | 5 | 3 | 5 | 2 | 3 | 2 | 2 |
 2. RTA | 2 | 5 |  | 4 |  | 3 | 5 | 3 | 3 |
 3. Globulin | 3 |  |  | 5 |  |  |  | 5 | 5 |
 4. Amylase | 4 |  |  |  |  |  |  |  |  |
 5. Cytopenia | 5 |  |  |  |  |  |  |  |  |
Immuno-modulation used | MTX IAS LF TOF | MTX IAS | MF | MTX IAS MF | IVIG MF | TOF | AZA | AZA | MF |
ESSDAI Score at onset | 10 | 9 | 6 | 8 | 6 | 5 | 4 | 9 | 5 |