Table 1 (abstract P313). Spectrum of Rheumatic Diseases in 4065 children presented first time at our centre
From: Proceedings of the 27th European Paediatric Rheumatology Congress (PReS 2021)
Disease (Number of Patients) | Number of Patients(%) |
|---|---|
Juvenile Idiopathic Arthritis-JIA Enthesitis-Related Arthritis(578)>Systemic-JIA(276)>Oligoarticular JIA(186) > Polyarticular-JIA(116)>Undifferentiated-JIA(21)>Psoriatic-JIA(6) ? JIA(21) Inflammatory Bowel Disease-associated arthritis(23) | 1227(30%) |
Connective Tissue Diseases-CTDs Systemic Lupus Erythematosus(208)>Juvenile Dermatomyositis(61) >Scleroderma(18)>Undifferentiated-CTD(14)>Overlap Syndrome(14)> Mixed-CTD(9)>Sjogren’s syndrome (2) | 326(8%) |
Primary Vasculitides Kawasaki Disease(188) >IgA-Vasculitis(126)>Behcet’s Disease(19)> Polyarteritis Nodosa(16)>Takayasu Arteritis(5)>Small Vessel Vasculitis(5) | 359(9%) |
Inflammatory Eye Diseases : Uveitis(51)>Scleritis(3)>Episcleritis(2) | 56(1.5%) |
Reactive Arthritides and Infections Reactive-Arthritis(128),Streptococcal-associated infections(77) including PSRA(10) and ARF(15), Viral infections(62), Transient synovitis of Hip(39), Tuberculosis including poncet’s disease(47) & Bone-Joint infections(17) | 370(9%) |
Non–Inflammatory Musculoskeletal Diseases Mechanical conditions(152)>Pain-amplification(58)>Fibromyalgia(52)>Joint Hypermobility(19)>Reflex Sympathetic dystrophy(11) | 292(7%) |
Miscellaneous Diseases | 537(13.5%) |
 - Ø ?Primary Immunodeficiencies | 28 |
 - Ø ?Autoinflammatory Syndromes | 34 |
 - Ø Non-specific inflammatory conditions | 45 |
 - Ø Suspected IGG4-related disease | 5 |
 - Ø Sarcoidosis | 9 |
 - Ø Skin Diseases | 101 |
 - Ø Haematological disorders including malignancy | 76 |
 - Ø Metabolic/Endocrine Disorders including Vitamin D Deficiency | 59 |
 - Ø Genetic diseases | 38 |
 - Ø Neuromuscular disorders | 41 |
 - Ø Secondary Vasculitis | 31 |
 - Ø Pyrexia of Unknown Origin | 52 |
 - Ø Psychiatric disorders | 18 |
Children with no abnormality detected | 414(10%) |
Children whose diagnosis has not been made due to single visit | 484(12%) |