Table 5 Comparison of findings to previous small case series on paediatric ECDS/PRS
From: Magnetic resonance imaging findings in children with Parry-Romberg syndrome and en coup de sabre
Doolittle | Maloney | Chiu | Knights | ||
|---|---|---|---|---|---|
Number of patients | 23a | 10 | 19a | 14 | |
MRI abnormalities | Any | 48%b | 100% | 32% | 50% |
White matter hyperintensity | 35% | 90% | 16% | 43% | |
Dystrophic calcification | 4% | 50% | 5% | 36% | |
Contrast enhancement | 0% | 20% | 0% | 36% | |
Sulcal crowding | 4% | 0% | 11% | 21% | |
Cavernomata | 0% | 0% | 0% | 7% | |
Porencephaly | 4% | 40% | 0% | 7% | |
Other | 17% | 0% | 5% | 0% | |
Neurological manifestations | Neurological symptoms | 43%c | 80% | 42% | 64% |
Seizures | 13% | 50% | 16% | 43% | |
Headaches | 26% | 50% | 16% | 29% | |
Other | 9% | 10% | 42% | 50% | |