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Table 5 Comparison of findings to previous small case series on paediatric ECDS/PRS

From: Magnetic resonance imaging findings in children with Parry-Romberg syndrome and en coup de sabre

  Doolittle Maloney Chiu Knights
Number of patients 23a 10 19a 14
MRI abnormalities Any 48%b 100% 32% 50%
White matter hyperintensity 35% 90% 16% 43%
Dystrophic calcification 4% 50% 5% 36%
Contrast enhancement 0% 20% 0% 36%
Sulcal crowding 4% 0% 11% 21%
Cavernomata 0% 0% 0% 7%
Porencephaly 4% 40% 0% 7%
Other 17% 0% 5% 0%
Neurological manifestations Neurological symptoms 43%c 80% 42% 64%
Seizures 13% 50% 16% 43%
Headaches 26% 50% 16% 29%
Other 9% 10% 42% 50%
  1. aOnly children with MRI during childhood included
  2. bBilateral findings common
  3. cOnly diagnosed after neurological review
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