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Table 1 Clinical and laboratory findings

From: Salivary gland ultrasound in the diagnostic workup of juvenile Sjögren’s syndrome and mixed connective tissue disease

 

pjSS (n = 9)

sjSS (n = 6)

sJSS MCTD (n = 10)

“Sicca symptoms”

n = 9 (100%)

n = 3 (50%)

n = 9 (90%)

Glandular swelling

n = 7 (77.8%)

n = 3 (50%)

n = 5 (50%)

Glandular pain

n = 4 (44.4%)

n = 2 (33.3%)

n = 6 (60%)

Affected Glandulae submandibulares

n = 8 (88.8%)

n = 5 (83.3%)

n = 10 (100%)

Renal manifestations

n = 0

n = 1 (16.6%)

n = 0

Articular

n = 7 (78%)

n = 6 (100%)

n = 10 (100%)

Peripheral nervous system

n = 1 (11.1%)

n = 0

n = 0

Cutaneous

n = 5 (55.5%)

n = 5 (83.3%)

n = 6 (60%)

Fatigue

n = 8 (88.8%)

n = 6 (100%)

n = 9 (90%)

Fever

n = 3 (33.3%)

n = 4 (66.6%)

n = 6 (60%)

ESSDAI (mean)

19.2 (range 7–35)

21.3 (range 10–44)

24.1 (range 3–72)

Remarkable

CRP/ ESR

(C-reactiv-protein/ erythrocyte sedimentation rate)

n = 8 (88.8%)

n = 4 (66.6%)

n = 4 (40%)

anti-Ro antibody +

n = 9 (100%)

n = 4 (66.6%)

n = 1 (10%)

anti-La antibody +

n = 8 (88.8%)

n = 4 (66.6%)

n = 0