Table 2 Demographic data of IRPA patients
Palindromic Rheumatism (PA) | Recurrent synovitis of the hip (RSH) | |
|---|---|---|
The mean age (years) | 10.12 | 10.33 |
Age at diagnosis (years) | 6.5 | 4.6 |
Male/female (N) | 6/2 | 1/2 |
Duration of follow-up a (years) | 2.6 | 6.6 |
Number of episodes per year | 4.75 | 3 |
Attack intervals (mean) month | 3.1(n = 7) | 1.6 |
Variable(n = 1) | ||
Systemic symptoms during attacks (%) | 37.5% | 0 |
Morning stiffness during attacks (%) | 12.5% | 0 |
Join involvement | Hip(n = 1) | |
Knee(n = 3) | ||
Ankle(n = 3) | Hip(n = 3) | |
Variable(n = 1) | ||
Joint pattern | Monoarticular | Monoarticular |
Mutations | Non (n = 7) | A744S(Female) |
V726A(n = 1/male) | R761H(Female) | |
V726A(Male) | ||
Average duration of episodes | 3.5 days(n = 4) | |
2.3 h(n = 3) | 3.3 days | |
Variable(n = 1) |