From: 10th Congress of International Society of Systemic Auto-Inflammatory Diseases (ISSAID)
No | S | Age | Trigger | Disease | Therapy | Outcome | Observations |
---|---|---|---|---|---|---|---|
1. | F | 72 | Resp. Virus | IIM | life support (ICU); MP pulses; cyclosporine; immunoglobulins | survival | ARF; hypoC4 Atypical rash |
2. | F | 56 | Acute cholecystitis | PG | Life support (ICU); immunoglobulins; MP, CyA | survival | Â |
3. | F | 58 | viral | RA | MP, CyA, MTX | survival | Â |
4. | F | 46 | ? | SLE/SSj (Ro52) | MP, CyA | survival | Evolved to Systemic sclerosis |
5. | F | 49 | Q fever | SLE/SSj (Ro52) cryoglobulinemia | Life support (ICU); plasma exchange; MP, CyA | survival | TMHA; hypoC3, C4 |
6. | M | 23 | ? | PAN | MP, CyA | survival | Â |
7. | F | 25 | ? | SLE | MP, CyA | survival | Â |
8. | F | 57 | Resp. virus | inflammatory idiopathic myopathy | MP pulses; CyA, then Aza | survival | Atypical rash |