From: 10th Congress of International Society of Systemic Auto-Inflammatory Diseases (ISSAID)
Females/males, n | 5/6 |
Mean age, years | 46,2±12,2 |
Clinical onset, n(%) | |
 Heart failure (LV-EF<55%) | 8(72.7) |
 Chest pain | 2(18.2) |
 Dyspnea | 1(9.1) |
NYHA class III-IV, n(%) | 8(72.7) |
EBM classification*, n(%) | |
 i-DCM | 6(54.5) |
 Acute/active/chronic VNM | 3(27.3)/1(9.1)/1(9.1) |