Table 1 (abstract P2049). Clinical features of patients with undifferentiated recurrent fevers compared to PFAPA syndrome
From: 10th Congress of International Society of Systemic Auto-Inflammatory Diseases (ISSAID)
Clinical features | Our cohort (34 patients) | Thomas et al. (82 patients) | Hofer et al. (301 patients) | Batu et al. (131 patients) | Pehlivan et al. (359 patients) | P value |
|---|---|---|---|---|---|---|
Mean duration of episodes (days; ±SD) | 5.9 ± 1.4 | NR | NR | NR | 4.0 ± 3.1 | <.0001 |
Median interval between episodes (weeks; ±SD) | 3.0 ± 0.3 | NR | NR | NR | 3.3 ± 1.5 | NS |
Abdominal pain | 17 (50) | 40 (49) | 136 (45) | 60 (46) | 102 (29) | NS |
Arthritis | 7 (21) | NR | 8 (3) | NR | 7 (0) | <.0001 |
Skin rash | 11 (32) | 7 (9) | 38 (13) | 7 (5) | NR | <.0001 |
Pharyngotonsillitis | 13 (38) | 59 (72) | 271 (90) | 126 (96) | 359 (100) | <.0001 |
Cervical lymphadenopathy | 6 (18) | 72 (88) | 236 (78) | 70 (53) | 215 (60) | <.0001 |
Oral aphthosis | 13 (38) | 57 (70) | 171 (57) | 56 (43) | 317 (88) | <.0001 |
Response to colchicine | 14/18 (78) | 0/1 (0) | NR | 5/11 (45) | 24/45 (53) | NS |