From: 10th Congress of International Society of Systemic Auto-Inflammatory Diseases (ISSAID)
 | Patient 1 | Patient 2 | Patient 3 |
---|---|---|---|
Age at 1st evaluation (years) | 14.3 | 7.8 | 4.9 |
Sex | F | F | M |
Clinical features | Recurrent fever, recurrent infection, vasculitis, skin rash, musculoskeletal pain | Hemolitic anemia,thrombocytopenia, HLH, vasculitis, recurrent infections, recurrent fever, arthritis, skin rash, gastrointestinal involvement | Recurrent fever, skin rash, vasculitis, arthritis, musculoskeletalpain |
SAA | 13-23 | 27,5-76,4 | 20 |
Zinchemia(mcg/dl) (n.v. 80-125) | 132-143 | 102-233 | 147 |
Serum MRP8/14 (ng/ml) (n.v. < 2900) | 22431 | 10383 | 10363 |