From: Proceedings of the 25th European Paediatric Rheumatology Congress (PReS 2018)
Sex | %48.8 male (n=39)Â Â Â Â Â %51.2 female (n=41) |
Onset of Symptoms (year) | 4.41 (0.16-17) |
Diagnosis time (year) | 7 (0.66-16) |
Family History of Rheumatic Disorders | %26.25 (n=21) |
Receiving Steroid Treatment | %37.5 (n=30) |
Types of MEFV mutations | 27.5% (n=22) MEFV mutation (+) 63.6% (n= 14) exon-10 mutations 54.5% (n=12) have M694V mutations 31.8% (n=7) have M694V homozygous |
ANA positivity | 27.5 (n=22) |
Infection and malignancy after treatment | Tuberculosis infection (n=1) Varicella zoster (n=1) Recurrent upper respiratory tract infections (n=2) Acute Lymphoblastic Leukaemia (n=1) |
Need of Tuberculosis Prophylaxis | %26.25 (n=21) |
Mean Remission Time (months) | 2.00 (1-18) |