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Table 1 Clinical presentations reported in literatures

From: Pigmented villonodular synovitis in pediatric population: review of literature and a case report

Clinical presentation

Number of patients

Age (years)

Sex

Treatment (OSa/ASb)

Follow up

Recurrence

Authors

Knee pain and swelling

21

1–15 (mean 9.1)

10 Mc, 11 Fd

12 OS, 7 AS, 1 OS + AS, 1 injection

5 month-2 years

None

Baroni [3], Neubauer [12], Bruns [11], Jawadi [5], Deepak [14], Hong [6], Saulsburg [7], Jha [9], Maric [15], Nizam [13]

Painless swelling of knee

1

5

1 M

AS

2 years

None

Van Emelen [10]

Politeal cyst

1

12

1 M

OS + AS

Meehan [8]

Foot and ankle pain and swelling

4

3–14 (mean 10.3)

3 M 1 F

OS

6 month-2 years

None

Neubauer [12], Aghasi [24], Freedman [23], Kaneko [26]

Painless mass of foot and ankle

3

11–12 (mean 11.7)

1 M

2 F

OS

1–4 years

None

Zambakides [25], Sofier [21], Duncan [22]

Elbow

1

8

1 F

AS

Hsiu Su [19]

Non tender mass or swelling of elbow

2

6 (mean 6)

2 F

OS

2 years

None

Sekiya [18], Aydingoz [17]

Multifocal involvement

6

4.5–7 (mean 5.8)

1 M

5 F

OS

6 month-25 years

3 cases

Mukhopadhyay [28], Tavangar [27], Vedantam [29], Zhao [30], Walls [32], Leszczynski [31]

Hip pain

1

7

1 F

AS + OS

Not reported

Higuchi [20]

Sacral joint involvement

1

12

1 F

OS

Kang [20]

Hand swelling

1

7

1 F

OS

7 year

1 case

Neubauer [12]

Average

3.8

8.9

F/M: 1.6/1

OS 69%, AS 21.5%, OS + AS 7%, Injection 2.5

4.9 years

9.5%

 
  1. aOpen synovectomy
  2. bArthroscopic synovectomy
  3. cMale
  4. dFemale