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Table 3 International classifications criteria for Behçet’s disease [1113] - Paediatric criteria for BD 2015

From: Behçet’s disease in children, an overview

Item

Description

Value/item

Recurrent oral aphtosis

At least 3 attacks/year

1

Genital ulceration

Typically with scar

1

Skin involvement

Necrotic folliculitis, acneiform lesions, erythema nodosum

1

Ocular involvement

Anterior or posterior uveitis, retinal vasculitis

1

Neurological signs

With the exception of isolated headaches

1

Vascular signs

Venous thrombosis, arterial thrombosis, arterial aneurysm

1

  1. Three of 6 items are required to classify a patient as having paediatric BD