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Table 2 International classifications criteria for Behçet’s disease [1113] - International criteria 2014

From: Behçet’s disease in children, an overview

Clinical manifestations

Description

Value/item

Oral aphthosis

 

2

Genital ulceration

 

2

Ocular signs

Anterior uveitis, posterior uveitis, retinal vasculitis

2

Skin lesions

Pseudo folliculitis, skin aphthosis, erythema nodosum

1

Neurological manifestation

 

1

Vascular signs

Arterial thrombosis, Large vein thrombosis, phlebitis or superficial phlebitis

1

Positive pathergy test

(additional criteria)

1

  1. Behçet’s disease diagnosis is made if the score is ≥ 4