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Table 3 PRINTO diagnostic criteria for MAS in sJIA [21]

From: Evidence-based diagnosis and treatment of macrophage activation syndrome in systemic juvenile idiopathic arthritis

A patient with (suspected) sJIA with

 

 Fever and serum ferritin > 684 ng/ml

 

AND any 2 of the following

 

 Platelet count ≤181 × 109/L

 

 Aspartate aminotransferase (>48 U/L

 

 Triglycerides > 156 mg/dl

 

 Fibrinogen ≤360 mg/dl

 
  1. Laboratory abnormalities should not be otherwise explained by the patient’s condition, such as concomitant immune-mediated thrombocytopenia, infectious hepatitis, visceral leishmaniasis, or familial hyperlipidemia
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Pediatric Rheumatology

ISSN: 1546-0096