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Table 1 Provisional classification criteria for the classification of Juvenile Systemic Sclerosis [8].

From: Clinical characteristics of children with Juvenile Systemic Sclerosis: follow-up of 23 patients in a single tertiary center

Major criterion (Required)
   Proximal (to MCP/MTP joints) skin sclerosis/induration of the skin
Minor criteria (At least two required)
   Cutaneous Sclerodactyly
   Peripheral vascular Raynaud's phenomenon
  Nailfold capillary abnormalities
  Digital tip ulcers
   Gastrointestinal Dysphagia
  Gastro-esophageal reflux
   Cardiac Arrhythmias
  Heart failure
   Renal Renal crisis
  New onset arterial hypertension
   Respiratory Pulmonary fibrosis (HRCT/radiograph)
  Decreased DLCO
  Pulmonary arterial hypertension
   Neurologic Neuropathy
  Carpal tunnel syndrome
   Musculoskeletal Tendon friction rubs
  Arthritis
  Myositis
   Serologic Antinuclear antibodies
  SSc selective autoantibodies
  (anticentromere, anti-topoisomerase I (Scl 70), anti-fibrillarin, anti-PM-Scl, anti-fibrillin or anti-RNA polymerase I or III)