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Table 1

From: Autoinflammation and immunodeficiency

 

Autoinflammatory disease

Mixed disorder

Innate immunodeficiency

Adaptive immunodeficiency

example

Mevalonate kinase deficiency

HOIL1-deficiency

Chronic granulomatous disease

Common Variable immunodeficiency

Rag1 deficiency

feature

Serious bacterial infections

Recurrent fever and humoral immunodeficiency

Sterile granulomata

Sterile granulomata