| Autoinflammatory disease | Mixed disorder | Innate immunodeficiency | Adaptive immunodeficiency |
---|---|---|---|---|
example | Mevalonate kinase deficiency | HOIL1-deficiency | Chronic granulomatous disease | Common Variable immunodeficiency Rag1 deficiency |
feature | Serious bacterial infections | Recurrent fever and humoral immunodeficiency | Sterile granulomata | Sterile granulomata |