Time / Disease course | 3 Years of age and below at onset n = 19 | Above 3 years of age at onset n = 59 | Total patients | p-value |
---|---|---|---|---|
1 Year | ||||
Persistent muscle weakness | 5/19 (26%) | 22/59 (37%) | 78 | 0.4612 |
Persistent rash | 6/19 (31%) | 32/59 (54%) | 78 | 0.1261 |
Elevated muscle enzymes | 0/19 (none) | 15/59 (25%) | 78 | 0.018 |
5 Years | 78 | |||
Active disease | 1 (9%) (8/19 patients were discharged/lost followup) | 15 (35.7%) (17/59 patients were discharged/lost followup) | 53 | 0.015 |
10 years | ||||
Active disease | 1 (9%) (8/19 patients were discharged/lost followup) | 14 (45.1%) (28/59 patients were discharged/lost followup) | 42 | 0.011 |