Figure 2
From: Joint contractures in the absence of inflammation may indicate mucopolysaccharidosis
Physical and Radiographic Appearance of Hands in MPS I versus Juvenile Idiopathic Arthritis. The images on the left depict typical findings in MPS I - the curled "claw hand," abnormal metacarpal bones, proximal widening of phalanges, and the V-shaped deformity of the distal ulna and radius, particularly evident in severe MPS I. In contrast, the images on the right of a child with juvenile arthritis show the typical joint swelling and erosive bone lesions. Photos courtesy of J. Edmond Wraith, Rolando Cimaz, and Bianca Link.