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Table 2 Analysis of complement system activity

From: The identification of a novel splicing mutation in C1qB in a Japanese family with C1q deficiency: a case report

Hemolytic activity

NHS

Patient serum

Reference value

CH50 (U/ml)

125

0

90ā€“160

(NHS %)

100%

0%

Ā 

ACH50 (U/ml)

18.5

18.9

Ā 

(NHS %)

100%

102%

70ā€“130%

C1 activity (U/ml)

1450

100

Ā 

(NHS %)

100%

7%

70ā€“130%

C2 activity (U/ml)

400

360

Ā 

(NHS %)

100%

90%

70ā€“130%

C4 activity (U/ml)

2000

1600

Ā 

(NHS %)

100%

80%

70ā€“130%

  1. NHS normal human serum, ACH50 alternative complement pathway activity.