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Table 2 Clinical features of 39 patients with primary Sjögren’s syndrome diagnosed in childhood

From: Childhood-onset primary Sjögren’s syndrome in a tertiary center in China: clinical features and outcome

Symptoms & signs

N(%)

Glandular enlargement/recurrent parotitis

10 (25.6)

Dry mouth + dry eyes

2 (5.1)

Isolated dry mouth or dry eyes

7 (17.9)

Fever

12 (30.8)

Arthralgia

7 (17.9)

Arthritis

1 (2.6)

Skin involvement

20 (51.3)

Rash

12 (30.8)

Purpura

8 (20.5)

Hematological involvement

14 (35.9)

Leukopenia

7 (17.9)

Thrombocytopenia

6 (15.4)

Anemia

4 (10.3)

Hepatic involvement

13 (33.3)

Lymphadenopathy

9(23.1)

Renal involvement

8 (20.5)

RTA

4 (10.3)

Proteinuria

4 (10.3)

Renal impairment

3 (7.7)

Interstitial pneumonia

3 (7.7)

Neurological involvement

1 (2.6)

Hypokalemia

4 (10.3)

Fatigue

1 (2.6)

Raynaud phenomenon

1 (2.6)