Table 1 Epidemiological features and criteria fulfillment of 39 patients with primary Sjögren’s syndrome diagnosed in childhood
Variable | Patients diagnosed with childhood-onset pSS (n = 39) |
|---|---|
Gender and age | |
Female(%) | 31(79.5) |
Age at diagnosis (yrs)/Median(range) | 10.9 (6.3, 15.0) |
Age at initial sign/symptom (yrs)/Median(range) | 9.2 (4.7, 14.5) |
Diagnosis delayed time (mths) /Median(range) | 6.5 (0.4, 72.9) |
Classification criteria | |
AECG criteria | 27 (69.2) |
ACR/EULAR criteria | 38 (97.4) |
Proposal juvenile pSS criteria | 35 (89.7) |
AECG or ACR/EULAR | 38 (97.4) |
AECG or Proposal juvenile pSS criteria | 37 (94.9) |
ACR/EULAR or Proposal juvenile pSS criteria | 39 (100) |