Table 2 Extrapolated JIA prevalence and incidence (n and rate per 100,000 population in Germany) in 2018 by ILAR category, with 95% confidence intervals

2018 Prevalence

WIG2

InGef

JIA

ILAR Categories

n extrapolated (Germany) (95% LCI-RCI)

WIG2

Adjusted rates /100,000 (95% LCI-RCI)

WIG2

n extrapolated (Germany) (95% LCI-RCI)

InGef

Adjusted rates /100,000 (95% LCI-RCI)

InGef

ALL

13,938 (12,792–15,161)

133 (122–145)

17,552 (16,391–18,774)

168 (157–179)

1

sJIA

924 (647–1283)

9 (6–12)

931 (679–1246)

9 (6–12)

2

oligoJIA

7330 (6503–8236)

70 (62–79)

9495 (8646–10,405)

91 (83–99)

3

RF- polyJIA

3218 (2678–3837)

31 (26–37)

4052 (3504–4661)

39 (33–45)

4

RF + polyJIA

375 (210–624)

4 (2–6)

888 (643–1197)

8 (6–11)

5

jPsA

251 (120–466)

2 (1–4)

579 (384–837)

6 (4–8)

6

ERA-JIA

932 (656–1288)

9 (6–12)

1010 (748–1336)

10 (7–13)

7

UA

5109 (4423–5873)

49 (42–56)

5893 (5228–6619)

56 (50–63)

2018 Incidence

WIG2

InGef

JIA ILAR Categories

n extrapolated (Germany) (95% LCI-RCI)

WIG2

Adjusted rates /100,000 (95% LCI-RCI)

WIG2

n extrapolated (Germany) (95% LCI-RCI)

InGef

Adjusted rates /100,000 (95% LCI-RCI)

InGef

ALL

3575 (2995–4239)

34 (29–41)

6277 (5573–7046)

60 (53–67)

1

sJIA

193 (78–402)

2 (1–4)

349 (199–568)

3 (2–5)

2

oligoJIA

1311 (966–1742)

13 (9–17)

2860 (2391–3394)

27 (23–32)

3

RF- polyJIA

472 (275–760)

5 (3–7)

1024 (752–1362)

10 (7–13)

4

RF + polyJIA

-

-

437 (267–675)

4 (3–6)

5

jPsA

-

-

305 (167–513)

3 (2–5)

6

ERA-JIA

339 (181–586)

3 (2–6)

434 (265–671)

4 (3–6)

7

UA

1034 (731–1423)

10 (7–14)

1634 (1285–2049)

16 (12–20)