From: Proceedings of the 28th European Paediatric Rheumatology Congress (PReS 2022)
 | MAS (N=54) | sHLH (N=48) | sJIA (N=4) | MAS vs sHLH | MAS vs sJIA | sHLH vs sJIA |
---|---|---|---|---|---|---|
Ferritin (ng/ml) | 4755 (1816-10988) | 4098 (2075-16867) | 717 (335-2313) | 0.77 | <0.0001 | <0.0001 |
Platelet count (x10^9/l) | 199 (107-314) | 97 (47-184) | 450 (343-570) | 0.0003 | <0.0001 | <0.0001 |
AST (U/L) | 85 (51-146) | 150 (51-340) | 30 (22-44) | 0.06 | <0.0001 | <0.0001 |
Triglycerides (mg/dl) | 188 (148-263) | 226 (166-381) | 105 (75-139) | 0.11 | <0.0001 | <0.0001 |
Fibrinogen (mg/dl) | 337 (222-433) | 228 (137-331) | 572 (482-692) | 0.003 | <0.0001 | <0.0001 |
LDH (U/L) | 965 (679-1369) | 1255 (701-2748) | 587 (365-724) | 0.10 | <0.0001 | <0.0001 |
CXCL9 (pg/ml) | 2236 (675-9670) | 4159 (1880-10016) | 300 (300-1979) | 0.14 | <0.0001 | <0.0001 |
Neopterin (ng/ml) | 9.4 (5.0-16.2) | 20.3 (9.6-35.0) | 4.2 (3.0-7.2) | 0.0018 | <0.0001 | <0.0001 |
IL-18 (pg/ml) | 170338 (83277-287152) | 11787 (21881120) | 36764 (8958-82714) | <0.0001 | <0.0001 | 0.19 |