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Table 2 Clinical and laboratory features of patients with CD and JIA

From: In a large Juvenile Idiopathic Arthritis (JIA) cohort, concomitant celiac disease is associated with family history of autoimmunity and a more severe JIA course: a retrospective study

 

Patient 1

Patient 2

Patient 3

Patient 4

Patient 5

Patient 6

Patient 7

Patient 8

Sex

F

F

M

M

F

F

F

F

Current age (years)

16.5

16.6

13.8

8.4

14.1

21.6

13.5

12.1

JIA subtype

Polyarticular

Undifferentiated

Systemic

Oligoarticular

Oligoarticular

Undifferentiated

Polyarticular

Undifferentiated

Age of JIA onset (years)

4.3

4.1

5

6.5

4.5

3.4

13

3

ANA ( ±)

-

 + 

 + 

-

 + 

-

-

-

Follow-up duration (years)

12.2

12.5

8.8

1.9

9.6

15.2

0.5

9.1

Age at CD diagnosis (years)

5

14.6

10.9

6.10

5.2

3.6

9.7

3.9

Anti-tTG (fold increase over ULN)

125

10

2.3

11

7.5

1.8

7.6

3

EMA ( ±)

 + 

 + 

-

 + 

 + 

 + 

 + 

 + 

Small intestinal biopsy

 + 

n.d.

 + 

 + 

 + 

 + 

n.d.

 + 

Marsh classification

T3b\c

n.d.

T3c

T3c

T3c

T3b

n.d.

T0

HLA-DQ2\-DQ8

n.d.

DQ2.5

DQ2 and DQ8

n.d.

n.d.

n.d.

n.d.

DQ2

Gastrointestinal symptoms

No

No

Yes

No

No

No

Yes

Yes

Extra-intestinal symptoms of CD

No

No

Yes

No

No

No

Yes

No

JIA therapy at CD diagnosis

NSAID

ADA

PDN

INDO; CsA;

TCZ

NSAID

MTX

MTX

NA

NAa

Relapse upon GFD

Yes

Yes

No

Yes

Yes

Yes

NA

Yes

Positive family history

of autoimmune disease

No

Yes

Yes

Yes

Yes

Yes

Yes

Yes

Family history of autoimmune disease specifics

NA

Psoriasis

Rheumatoid arthritis, type 1 diabetes

Thyroiditis

Thyroiditis, vitiligo

Psoriasis

Psoriasis, CD

Psoriasis

Co-occurrence of other autoimmune disorders

No

Uveitis

No

No

No

No

No

Uveitis

  1. NA Not Applicable, nd not done, CD Celiac Disease, JIA Juvenile Idiopathic Arthritis, ANA Antinuclear Antibody, Anti-tTG Anti-transglutaminase antibodies IgA, ULN Upper Limit of Normal, EMA anti-Endomysial Antibodies, HLA Human Leukocyte Antigen, GFD Gluten Dree Diet, NSAID Non-Steroidal Anti-inflammatory Drugs, ADA Adalimumab, PDN Prednisone, INDO Indomethacin, CsA Cyclosporin, TCZ Tocilizumab, MTX Methotrexate,
  2. aPatient 8 was off-therapy at CD diagnosis