Table 1 Demographics and Clinical Characteristics Demographics and clinical characteristics of the study cohort. All values are medians (interquartile range [IQR], range of values) unless otherwise indicated

Female (n)

10 (38%)

Age, years

12.5 (3.8, 7–17)

BMI, kg/m²

20.1 (5.4, 14.2–34.2)

Age at diagnosis, years

7.0 (5.8, 0.75–12.0)

Years since diagnosis

3.0 (6.5, 0–14.0)

Medications^a (n)

 None

8 (31%)

 Methotrexate

15 (58%)

 Calcium/Vitamin D/Folic Acid

14 (54%)

 Hydroxychloroquine

3 (12%)

 IVIG

2 (8%)

 MMF

1 (4%)

 Other

6 (24%)

 CHAQ Disability Index (0–3)

0 (0.125, 0–2.125)

 Patient Global Assessment (0–10)

0.3 (1.3, 0–8.4)

 Physician Global Assessment (0–10)

1.4 (3.9, 0–8.0)

 Nailfold Capillaroscopy, n/mm, [mean (SD)]

5.5 (0.8)

 CMAS (0–52)

52 (4.5, 27–52)

 MMT-8 (0–80)

80 (7.8, 55–80)

 Squat Test, n/30 s

22 (7, 9–30)

Wingate Test

 Peak Power (watts)

371 (204, 119–645)

 Relative Peak Power (watts/kg)

6.2 (2.4, 4.2–9.7)

 Fatigue Index (%)

50.4 (18.8, 33.6–102.6)

 Average Power (watts/kg)

4.5 (2.2, 2.7–7.3)