From: Proceedings of the 27th European Paediatric Rheumatology Congress (PReS 2021)
 | MAS (N=52) | sHLH (N=48) | sJIA (N=40) | MAS vs sHLH | MAS vs sJIA | sHLH vs sJIA |
---|---|---|---|---|---|---|
Ferritin (ng/ml) | 4593 (1770-10842) | 4098 (2075-16867) | 728 (335-2786) | 0.72 | <0.0001 | <0.0001 |
Platelet count (x10^9/l) | 200 (114-310) | 97 (47-184) | 449 (275-559) | 0.0003 | <0.0001 | <0.0001 |
AST (U/L) | 86 (51-149) | 150 (51-340) | 33 (23-46) | 0.07 | <0.0001 | <0.0001 |
Triglycerides (mg/dl) | 188 (148-286) | 226 (166-381) | 108 (78-140) | 0.11 | <0.0001 | <0.0001 |
Fibrinogen (mg/dl) | 330 (225-437) | 228 (137-331) | 565 (441-691) | 0.0018 | <0.0001 | <0.0001 |
LDH (U/L) | 975 (666-1446) | 1255 (701-2748) | 599 (407-724) | 0.11 | <0.0001 | <0.0001 |
CXCL9 (pg/ml) | 1728 (798-11507) | 4159 (1880-10016) | 300 (300-1989) | 0.15 | 0.0010 | <0.0001 |
Neopterin (ng/ml) | 9.4 (4.9-16.0) | 20.3 (9.6-35.0) | 4.3 (3.0-7.4) | 0.0023 | <0.0001 | <0.0001 |
IL-18 (pg/ml) | 159833 (50000-250000) | 13640 (2230-83909) | 36764 (8958-82714) | <0.0001 | <0.0001 | 0.16 |