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Table 1 (abstract P146) . Laboratory parameters and cytokine levels during disease course

From: Proceedings of the 27th European Paediatric Rheumatology Congress (PReS 2021)

 

Range

26/04/2017

19/02/2018

13/06/2018

24/02/2020

08/04/2020

22/04/2021

  

Onset primary HLH

Remission after emapalumab

Onset of liver involvement

sJIA critria and full-blown MAS

Start emapalumab

1 year after emapalumab

GB (10^3 /uL)

5.5-15

12,27

6,44

6,09

7,48

0,91

4,8

PLT (10^3 /uL)

150-450

46

438

206

64

11

207

Ferritin (ng/ml)

13-150

293.400

100

27

3.460

13.411

5

AST (UI/L)

<32

578

31

851

733

432

32

IL-18 (pg/ml)

<300

>125.000

24.470

41.399

51.510

50.000

12.370

CXCL9 (pg/ml)

<612

379.642

710

546

15.163

193.783

<50

Neopterin (ng/ml)

<2,5

11,05

2,97

4,20

16,3

8,9

0,75