From: Proceedings of the 27th European Paediatric Rheumatology Congress (PReS 2021)
 | N° of patients | Survivors | Died | Mortality rate cause-specific (%) | Mortality rate overall (%) |
---|---|---|---|---|---|
All sHLH | 82 | 60 | 22 | - | 26.8% |
Secondary to rheumatic/inflammatory disease | 21 | 15 | 6 | 28.6% | 7.3% |
- SLE | 4 | 3 | 1 | 25% | 0.01% |
- Other rheumatic/inflammatory diseases | 17 | 12 | 5 | 29% | 6.1% |
sHLH (excluding rheumatic/inflammatory diseases) | 61 | 45 | 16 | 26.2% | 19.5% |
- Infections | 39 | 33 | 6 | 15.4% | 7.3% |
- Others | 8 | 2 | 6 | 75.0% | 7.3% |
- Unknown | 14 | 10 | 4 | 28.6% | 4.9% |