From: Proceedings of the 27th European Paediatric Rheumatology Congress (PReS 2021)
Characteristics | Patients (N: 24 (% of N) or median (min-max)) |
---|---|
Male gender | 16 (66.7) |
Age at disease onset, years | 9.75 (1.50-16.00) |
Age at diagnosis, years | 11.04 (3.50-16.17) |
Total clinical score | 40.00 (26.00-54.00) |
Normal blood cell count | 17 (70.8) |
Presence of MEFV mutation (n: 22) | 7 (31.8) |
Bone biopsy and/or bone marrow aspiration | 16 (66.7) |
Whole-body imaging findings | |
 Total number of lesions | 6.50 (2.00-17.00) |
 Multifocal lesions | 24 (100) |
 Symmetric lesions | 18 (75) |
 Lower extremity lesions | 22 (91.7) |
 Vertebral lesions | 12 (50) |
 Sacroiliitis | 9 (37.5) |
Treatment | |
 NSAID | 24 (100) |
 Corticosteroids | 6 (25) |
 Colchicine | 6 (25) |
 Biphosphonate | 4 (16.7) |
 Methotrexate | 2 (8.3) |
 Anti-TNF agents | 8 (33.3) |