From: Proceedings of the 27th European Paediatric Rheumatology Congress (PReS 2021)
 | Girl A, 6 years | Boy B, 3 years 9 months | Literature data |
---|---|---|---|
Sex (M / F) | F | M | 1,3 / 1 |
Age of onset | From birth | From birth | 1-24 months |
Age of diagnosis (years) | 4 | 1 | - |
Camptodactyly | + | + | 68%-100% |
Coxa vara | + | + | 70%-100% |
Polyarthritis Pain, morning stiffness | + | + | 45,7-100% |
Pericarditis/ Pleurisy | + | + | 7,6-50% |
Laboratory activity | - | - | Rarely |
No | No | No | |
Therapy/Response to therapy: | Â | Â | Traditional antirheumatic therapy is not effective. |
 Methotrexate | +/- | +/- | |
 GC per os | +/ partial | +/ partial | |
 Etanercept | +/ partial | - | |
 Tocilizumab | +/ partial | +/ partial |