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Table 2 Cardiac Abnormalities in JIA Cohort and subtype descriptions - 74 patients – 20 cardiac abnormalities occurrence in 17 (22.90%) patients

From: Frequency of Fabry disease in a juvenile idiopathic arthritis cohort

Features Total N (%) Presentation x JIA Subtype
Right Bundle Branch Block   4 polyarticular
10 (52.63) 1 systemic
  3 oligoarticular
  2 Entesitis-related
Mitral Valvar Prolapse   1 polyarticular
4 (20) 2 oligoarticular
Ventricular Hypertrophy   1 polyarticular -LV (conc.)
3 (15.78) 1 systemic - RV
  1 Oligoarticular + FD - LV (conc.)
Valvar Regurgitation:   Mitral: 1 Oligoarticular + FD
3 (15.78) Pulmonary: 1 Systemic
  Tricuspid: 1 Systemic
  1. Legends: LV Left Ventricle, RV Right ventricle, Conc concentric. The mitral regurgitation was a pathologic insufficiency with LV hypertrophy, while pulmonary and tricuspid regurgitations were physiologic