From: Frequency of Fabry disease in a juvenile idiopathic arthritis cohort
Features | Total N (%) | Presentation x JIA Subtype |
---|---|---|
Right Bundle Branch Block | 4 polyarticular | |
10 (52.63) | 1 systemic | |
3 oligoarticular | ||
2 Entesitis-related | ||
Mitral Valvar Prolapse | 1 polyarticular | |
4 (20) | 2 oligoarticular | |
Ventricular Hypertrophy | 1 polyarticular -LV (conc.) | |
3 (15.78) | 1 systemic - RV | |
1 Oligoarticular + FD - LV (conc.) | ||
Valvar Regurgitation: | Mitral: 1 Oligoarticular + FD | |
3 (15.78) | Pulmonary: 1 Systemic | |
Tricuspid: 1 Systemic |