Treatment | Total treated N | Response (R) / No Response (NR) | JIAU N = 14 | Idiopathic N = 12 | Sarcoidosis N = 2 | Behcet’s Disease N = 1 | Total N (%) | |
---|---|---|---|---|---|---|---|---|
Screening N = 11 | Pre-JIA diagnosis N = 3 | |||||||
Standard Initial Rx | 29 | R | 7 | 1 | 6 | 2 | 1 | 17 (58.6) |
NR | 4 | 2 | 6 | 0 | 0 | 12 (41.4) | ||
Azathioprine | 8 | R | 1 | – | 0 | – | – | 1 (12.5) |
NR | 3 | – | 4 | – | – | 7 (87.5) | ||
Mycophenolate Mofetil | 3 | R | 1 | – | 0 | – | – | 1 (33.3) |
NR | 1 | – | 1 | – | – | 2 (66.6) | ||
Infliximab | 6 | R | 1 | 0 | 1 | – | – | 2 (33.3) |
NR | 1 | 1 | 1 | – | – | 3 (50) | ||
Adalimumab | 8 | R | 1 | 2 | 4 | – | – | 7 (87.5) |
NR | 0 | 0 | 1 | – | – | 1 (12.5) | ||
Surgery: no. of children N (%) | 2 | 1 | 9 | 0 | 0 | 12 (41.4) | ||
No. of procedures | ||||||||
Cataract incl. Pars planar vitrectomy/ lensectomy | 2 | 1 | 10 | 0 | 0 | 13 | ||
Corneal chelation | 0 | 0 | 2 | 0 | 0 | 2 | ||
Evisceration | 0 | 0 | 1 | 0 | 0 | 1 |