Table 1 Etiologies of pediatric uveitis
From: Epidemiology of pediatric uveitis and associated systemic diseases
Etiology | Total N (%) | Categories | N (%) | Median age at uveitis diagnosis, y (IQR) | Systemic treatment, N (%) | Median follow-up, m (IQR) |
|---|---|---|---|---|---|---|
Idiopathic | 101 (65.2) |  |  | 13.0 (10.0–16.0) | 39 (38.6) | 16.0 (2.0–53.0) |
Systemic immune-mediated disease | 44 (28.4) | Juvenile idiopathic arthritis | 23 (14.8) | 11.0 (6.5–16.0) | 20 (87.0) | 72.0 (2.5–111.0) |
|  | Behçet disease | 10 (6.5) | 15.0 (13.3–16.8) | 9 (90.0) | 120.0 (67.5–132.0) | |
|  | Kawasaki disease | 3 (1.9) | 11.0 (11.0–12.0) | 3 (100) | 15.0 (14.5–33.5) | |
|  | Vogt–Koyanagi–Harada syndrome | 3 (1.9) | 16.0 (15.0–17.0) | 2 (66.7) | 36.0 (29.0–60.0) | |
|  | Tubulo-intestinal nephritis | 2 (1.3) | 11.5 (11.3–11.8) | 2 (100) | 49.5 (38.3–60.8) | |
| Â | Systemic lupus erythematosus | 1 (0.7) | 6 | 1 (100) | 180 | |
| Â | Kikuchi disease | 1 (0.7) | 17 | 1 (100) | 35 | |
| Â | Inflammatory bowel disease | 1 (0.7) | 13 | 1(100) | 42 | |
Syndrome confined primarily to the eye | 5 (3.2) | Trauma | 3 (1.9) | 12.0 (8.0–16.0) | 1 (33.3) | 9.0 (7.5–40.5) |
|  | Posner–Schlossman syndrome | 1 (0.7) | 18 | 1 (100) | 0.3 | |
| Â | Sympathetic ophthalmia | 1 (0.7) | 9 | 1 (100) | 3 | |
Masquerade syndrome | 4 (2.6) | Langerhans cell histiocytosis | 2 (1.3) | 13.0 (11.0–17.0) | 1 (50.0) | 95.5 (77.3–113.8) |
| Â | Acute lymphocytic leukemia | 1 (0.7) | 18 | 1 (100) | 60 | |
| Â | Hydroa vacciniforme-like lymphoma | 1 (0.7) | 6 | 1 (100) | 16 | |
Infection | 1 (0.7) | Varicella zoster virus | 1 (0.7) | 17 | 0 (0.0) | 21 |