From: Magnetic resonance imaging findings in children with Parry-Romberg syndrome and en coup de sabre
Demographics | Neurological disorders | Psychiatric disorders | Laboratory | ||||||||||||||||||||||||||||||||||||
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Age | Age at diagnosis | Ethnicity | Disease type | Sex | Any | Seizures | Headaches | Cranial nerve dysfunction | Any | Anxiety | ANA | ||||||||||||||||||||||||||||
< 14 | > 14 | p | < 7 | > 7 | p | White British | Other | p | ECDS | ECDS/PRS | p | M | F | p | Yes | No | p | Yes | No | p | Yes | No | p | Yes | No | p | Yes | No | p | Yes | No | p | Yes | No | p | ||||
Specific MRI changes | White matter high signal intensity | n = 6 | Yes | 4 | 2 | 0.59 | 4 | 2 | 0.59 | 3 | 3 | 0.18 | 2 | 4 | 0.63 | 2 | 4 | 0.63 | 6 | 0 | 0.031 | 5 | 1 | 0.026 | 2 | 4 | 1 | 2 | 4 | 0.16 | 2 | 4 | 1 | 1 | 5 | 1 | 3 | 2 | 1 |
No | 3 | 5 | 3 | 5 | 6 | 0 | 4 | 4 | 4 | 4 | 3 | 5 | 1 | 7 | 2 | 6 | 0 | 8 | 2 | 6 | 1 | 7 | 4 | 3 | |||||||||||||||
Dystrophic calcification | n = 5 | Yes | 3 | 2 | 1 | 4 | 1 | 0.27 | 3 | 2 | 0.52 | 2 | 3 | 1 | 2 | 3 | 1 | 5 | 0 | 0.1 | 4 | 1 | 0.1 | 2 | 3 | 1 | 1 | 4 | 1 | 2 | 3 | 1 | 1 | 4 | 1 | 2 | 2 | 1 | |
No | 4 | 4 | 3 | 5 | 6 | 1 | 4 | 4 | 4 | 4 | 4 | 4 | 2 | 6 | 2 | 6 | 1 | 7 | 2 | 6 | 1 | 7 | 4 | 3 | |||||||||||||||
Contrast enhancement | n = 5 | Yes | 3 | 2 | 1 | 4 | 1 | 1 | 3 | 2 | 1 | 2 | 3 | 0.52 | 2 | 3 | 1 | 5 | 0 | 1 | 4 | 1 | 0.52 | 2 | 3 | 1 | 1 | 4 | 1 | 2 | 3 | 1 | 1 | 4 | 1 | 2 | 2 | 1 | |
No | 4 | 1 | 3 | 2 | 4 | 1 | 4 | 1 | 3 | 2 | 4 | 1 | 2 | 3 | 2 | 3 | 1 | 4 | 1 | 4 | 0 | 5 | 2 | 2 | |||||||||||||||
Leptomeningeal enhancement | n = 4 | Yes | 2 | 2 | 0.5 | 3 | 1 | 1 | 2 | 2 | 0.5 | 2 | 2 | 1 | 1 | 3 | 0.52 | 4 | 0 | 1 | 3 | 1 | 0.57 | 2 | 2 | 1 | 1 | 3 | 1 | 2 | 2 | 0.5 | 1 | 3 | 0.4 | 2 | 2 | 1 | |
No | 5 | 1 | 4 | 2 | 5 | 1 | 4 | 2 | 4 | 2 | 5 | 1 | 3 | 3 | 2 | 4 | 1 | 5 | 1 | 5 | 0 | 6 | 2 | 2 | |||||||||||||||
Sulcal crowding | n = 3 | Yes | 1 | 2 | 1 | 2 | 1 | 1 | 1 | 1 | 0.45 | 1 | 2 | 1 | 1 | 2 | 1 | 2 | 1 | 1 | 1 | 2 | 1 | 1 | 2 | 1 | 1 | 2 | 0.4 | 1 | 2 | 1 | 0 | 3 | 1 | 2 | 1 | 1 | |
No | 6 | 5 | 5 | 6 | 8 | 2 | 5 | 6 | 5 | 6 | 7 | 4 | 5 | 6 | 3 | 8 | 1 | 10 | 3 | 8 | 2 | 9 | 5 | 4 | |||||||||||||||
Cavernomata | n = 1 | Yes | 1 | 0 | 1 | 1 | 0 | 1 | 1 | 0 | 1 | 0 | 1 | 1 | 1 | 0 | 0.43 | 1 | 0 | 1 | 1 | 0 | 0.43 | 0 | 1 | 1 | 0 | 1 | 1 | 0 | 1 | 1 | 0 | 1 | 1 | 0 | 0 | 1 | |
No | 6 | 7 | 6 | 7 | 8 | 3 | 6 | 7 | 5 | 8 | 8 | 5 | 5 | 8 | 4 | 9 | 2 | 11 | 4 | 9 | 2 | 11 | 7 | 5 | |||||||||||||||
Porencephaly | n = 1 | Yes | 1 | 7 | 1 | 1 | 0 | 1 | 1 | 0 | 1 | 0 | 1 | 1 | 0 | 1 | 1 | 1 | 0 | 1 | 1 | 0 | 0.43 | 0 | 1 | 1 | 0 | 1 | 1 | 0 | 1 | 1 | 0 | 1 | 1 | 0 | 1 | 0.42 | |
No | 6 | 0 | 6 | 7 | 8 | 3 | 6 | 7 | 6 | 7 | 8 | 5 | 5 | 8 | 4 | 9 | 2 | 11 | 4 | 9 | 2 | 11 | 7 | 4 |