From: Magnetic resonance imaging findings in children with Parry-Romberg syndrome and en coup de sabre
| Normal MRI | Abnormal MRI | p | ||||
|---|---|---|---|---|---|---|
| Patient demographics | Disease | ECDS | 4 | 2 | 0.59 | |
| ECDS/PRS | 3 | 5 | ||||
| Sex | M | 4 | 2 | 0.59 | ||
| F | 3 | 5 | ||||
| Additional clinical features | Any | Any | Yes | 5 | 7 | 0.46 |
| No | 2 | 0 | ||||
| Neurological | Any | Yes | 3 | 6 | 0.27 | |
| No | 4 | 1 | ||||
| Seizures | Yes | 1 | 5 | 0.1 | ||
| No | 6 | 2 | ||||
| Headaches | Yes | 2 | 2 | 1 | ||
| No | 5 | 5 | ||||
| Cranial nerve dysfunction | Yes | 0 | 2 | 0.46 | ||
| No | 7 | 5 | ||||
| Transient ischaemic attack | Yes | 0 | 1 | 1 | ||
| No | 7 | 6 | ||||
| Myoclonus | Yes | 0 | 1 | 1 | ||
| No | 7 | 6 | ||||
| Hyperaesthesia | Yes | 1 | 0 | 1 | ||
| No | 6 | 7 | ||||
| Gait disturbance | Yes | 0 | 1 | 1 | ||
| No | 7 | 6 | ||||
| Psychiatric disorder(s) | Any | Yes | 2 | 2 | 1 | |
| No | 5 | 5 | ||||
| Anxiety | Yes | 1 | 1 | 1 | ||
| No | 6 | 6 | ||||
| Depression | Yes | 0 | 1 | 1 | ||
| No | 7 | 6 | ||||
| OCD | Yes | 0 | 1 | 1 | ||
| No | 7 | 6 | ||||
| Visual hallucinations | Yes | 1 | 0 | 1 | ||
| No | 6 | 7 | ||||
| Cardiovascular | Any | Yes | 1 | 1 | 1 | |
| No | 6 | 6 | ||||
| Hypertension | Yes | 0 | 1 | 1 | ||
| No | 7 | 6 | ||||
| Bicuspid aortic valve | Yes | 1 | 0 | 1 | ||
| No | 6 | 7 | ||||
| Articular | TMJ dysfunction | Yes | 1 | 0 | 1 | |
| No | 6 | 7 | ||||
| Muscular | Myositis | Yes | 1 | 0 | 1 | |
| No | 6 | 7 | ||||
| Laboratory and other investigations | Autoantibodies | ANA | Yes | 3 | 4 | 1 |
| No | 3 | 2 | ||||
| Anti-smooth muscle | Yes | 0 | 1 | 0.4 | ||
| No | 3 | 1 | ||||
| RF | Yes | 0 | 1 | 0.33 | ||
| No | 4 | 1 | ||||
| ENA | Yes | 0 | 0 | 1 | ||
| No | 1 | 5 | ||||
| dsDNA | Yes | 0 | 0 | 1 | ||
| No | 3 | 4 | ||||
| Cerebrospinal fluid | Inflammatory infiltrate | Yes | 0 | 0 | 1 | |
| No | 0 | 3 | ||||
| Neurophysiology | EEG abnormality | Yes | 1 | 3 | 1 | |
| No | 0 | 1 | ||||