ANA n = 84 | CANA n = 27 | ANA n = 80a | CANA n = 26a | ||
---|---|---|---|---|---|
Age at diagnosis | 5.5 years | 7.4 years | |||
Symptoms before IL-1i | under IL-1i | ||||
Fever | 90% | 85% | 28% | 27% | |
Skin involvement | 71% | 81% | 25% | 33% | |
- Joint involvement* (arthritis/arthralgia) | 59 70% / 19 23% | 23 85% / 16 59% | 37 46% / 21 26% | 11 41% / 5 19% | |
- Abdominal | 30% | 70% | 13% | 26% | |
- Serositis | 17% | 11% | 4% | 4% | |
Duration of initial therapy to IL-1i | 15 months | 15 months | |||
Age at start of IL-1i | 6.8 years | 8.7 years | |||
Duration of IL-1i | 34 months | 16 months | |||
Disease course | |||||
MC | 7 (8%) | 0 (0%) | |||
PC | 36 (43%) | 14 (52%) | |||
PA | 41 (49%) | 13 (48%) | |||
Joint involvement* | polyarthritis 41 (49%) | 13 (48%) | 25 (31%) | 7 (27%) | |
oligoarthritis 18 (21%) | 8 (30%) | 12 (15%) | 4 (15%) | ||
arthralgia 19 (23%) | 16 (59%) | 21 (26%) | 5 (19%) | ||
none 6 (7%) | 0 (0%) | 22 (28%) | 10 (38%) |