Table 1 Clinical characteristics of patients, data is given as median and range
Number of patients, n | 19 |
male/female | 7/12 |
Age [years] | 14.0 (9–17) |
Duration of disease [years] | 4.0 (0–10) |
Diagnosis, n | |
JIA | 12 |
- psoriatic arthritis | 1 |
- polyarthritis | 5 |
- oligoarthritis | 4 |
- undifferentiated JIA | 1 |
- enthesitis associated arthritis | 1 |
other rheumatic diseases | 7 |
- mixed connective tissue disease | 1 |
- juvenile dermatomyositis | 1 |
- systemic autoimmune disorders of unspecified identity | 3 |
- chronic recurrent multifocal osteomyelitis | 1 |
- COPA-Syndrome | 1 |
Disease activity, n | |
active/inactive | 10/9 |
Therapy, ever, n | |
Methotrexate/Biologicals/None | 15/6/3 |
LCI | 8.03 (6.1–14.1) |
DLCO [% Hb corrected] | 81.0 (50–119) |
TLC [% predicted] | 91 (56–119) |