| Measure of Disease Activity | Median [IQR] | Patients with normal values* |
|---|---|---|
| CPK (U/L) | 95 [71, 153] | 19 (95%) |
| LDH (U/L) | 213 [176, 243] | 19 (95%) |
| AST (U/L) | 24 [22, 27] | 18 (90%) |
| Aldolase (U/L) | 6.4 [5.6, 7.3] | 19 (95%) |
| VWF antigen (%) | 119 [72, 149] | 12 (63%) |
| CMAS | 52 [50, 52] | 13 (65%) |
| DAS | 0 [0, 2] | 11 (55%) |