From: Clinical characteristics and poor predictors of anti-NXP2 antibody-associated Chinese JDM children
ID | gender | Age* | Duration | BMI (kg/m2) | First symptom | CMAS | Dysphagia/ Hoarseness/ Lower Voice | Ulcer/ Edema | max CK (U/L) | SF (μg/ml) | ANA/ Anti-Ro-52 | CD4/CD8 ratio | ILD | Gastro-intestinal | Treatment | Follow -up(m) | Clinical partial response at 3rd month | CMAS at the end of the follow-up | ||
---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|
Rash | Weakness | both | ||||||||||||||||||
1 | M | 8 | 1 | 18.1 | Y | 23 | N | N/N | 1794 | 67 | N/N | 2.01 | N | N | 1 + 2 + 0 + 0 + 0 | 41 | N | 52 | ||
2 | M | 1 | 42 | 15.6 | Y | 16 | N | N/N | Nd | 48 | Y/N | 1.54 | N | N | 1 + 2 + 0 + 0 + 0 | 49 | N | 45 | ||
3 | M | 8 | 1 | 19.5 | Y | 23 | Y | N/N | 3873 | 202 | Y/N | 0.83 | N | N | 1 + 1 + 0 + 0 + 0 | 47 | Y | 52 | ||
4 | F | 11 | 7 | 15.2 | Y | 25 | N | N/N | Nd | 97 | N/N | 2.25 | N | N | 1 + 4 + 0 + 0 + 0 | 60 | Y | 52 | ||
5 | F | 9 | 3 | 21.9 | Y | 47 | Y | N/N | 8138 | 120 | N/N | 1.68 | N | N | 1* + 2 + I + 0 + 1 | 16 | Y | 47 | ||
6 | F | 4 | 6 | 24.6 | Y | 22 | Y | N/N | 535 | 132 | N/N | 2.03 | N | N | 1* + 3 + I + 0 + 0 | 15 | Y | 52 | ||
7 | F | 4 | 6 | 15.7 | Y | 47 | N | N/N | 516 | 50 | N/N | 2.23 | N | N | 1* + 1 + I + 2 + 1 | 14 | N | 47 | ||
8 | M | 3 | 12 | 15.7 | Y | 22 | N | Y/N | Nd | 141 | N/N | 1.52 | N | N | 1 + 0 + 0 + 0 + 0? | Nd | Nd | Nd | ||
9 | F | 6 | Nd | Nd | Y | 23 | N | N/N | 757 | Nd | N/N | 2.18 | N | N | 1 + 2 + 0 + 0 + 0 | 14 | Y | 52 | ||
10 | M | 1 | 2 | 17.9 | Y | 4 | Y | N/N | 621 | 474 | Y/N | 2.07 | N | N | 1* + 2 + I + 0 + 0 | 16 | N | 47 | ||
11 | F | 7 | 1 | 22.6 | Y | 28 | N | N/N | 922 | 14 | N/N | 1.7 | N | N | 1 + 3 + 0 + 0 + 0 | 51 | N | 52 | ||
12 | F | 2 | 1 | 14.1 | Y | 8 | N | N/N | 582 | 193 | N/N | 2.08 | Y | N | 1* + 1 + I + 0 + 0 | 13 | Y | 52 | ||
13 | F | 6 | 1 | 18.2 | Y | 0 | Y | N/N | 3327 | 178 | N/N | 2.3 | Y | N | 1* + 3 + I + 0 + 0 | 18 | Y | 52 | ||
14 | F | 5 | 1 | 14.9 | Y | 8 | N | N/N | 3392 | 279 | Y/Y | 1.28 | N | N | 1* + 2 + I + 0 + 0 | 22 | Y | 49 | ||
15 | F | 4 | 3 | 16.4 | Y | 0 | N | N/N | 1010 | 227 | N/Y | 1.7 | N | N | 1* + 3 + I + 0 + 0 | 34 | Y | 47 | ||
16 | F | 6 | 1 | 16.2 | Y | 0 | Y | N/Y | 15,140 | 783 | N/Y | 1.93 | N | N | 1* + 2 + I + 0 + 1 | 16 | Y | 40 | ||
17 | F | 13 | 1 | 29.1 | Y | 6 | Y | Y/N | 1156 | 239 | Y/N | 1.25 | Y | N | 1* + 3 + I + 1 + 1 | 31 | Y | 47 | ||
18 | F | 1 | 4 | 16.6 | Y | 25 | N | N/N | 221 | 362 | N/N | 2.33 | N | N | 1* + 3 + I + 1 + 0 | 29 | N | 45 | ||
19 | M | 1 | 3 | 17.5 | Y | 0 | Y | Y/Y | 1096 | 347 | N/Y | 1.16 | Y | N | 1* + 3 + I + 0 + 1 | 28 | N | 18 | ||
20 | M | 1 | 3 | 15.3 | Y | 0 | Y | Y/Y | 2000 | 185 | Y/Y | 0.81 | N | N | 1* + 4 + I + 1 + 1 | 12 | N | 33 | ||
21 | F | 1 | 3 | 13.9 | Y | 2 | Y | Y/Y | 1250 | 323 | Y/N | ND | N | Y | 1* + 5 + I + 1 + 1 + ASCT | 12 | N | 27 | ||
22 | F | 5 | 1 | 13.3 | Y | 0 | Y | Y/Y | 10,064 | 584 | Y/N | 0.75 | Nd | Y | 1* + 3 + I + 0 + 0 | 0.1 | Y | / | ||
23 | F | 3 | 2 | 13.6 | Y | 5 | Y | Y/Y | Nd | Nd | Y/N | Nd | N | Y | 1* + 3 + I + 0 + 0 | 43 | N | / | ||
24 | M | 4 | 1 | 16.1 | Y | 5 | Y | Y/Y | 118 | 132 | Y/N | 1.14 | Y | Y | 1* + 5 + I + 1 + 0 | 12 | N | / | ||
25 | F | 6 | 1 | 11.3 | Y | 2 | Y | Y/Y | 6457 | 416 | Y/Y | 0.68 | Y | Y | 1* + 3 + I + 0 + 0 | 4 | N | / | ||
26 | F | 9 | 1.5 | 12.8 | Y | 2 | Y | Y/Y | 3178 | 1566 | Y/Y | 1.74 | Y | Y | 1* + 1 + I + 1 + 0 | 1 | N | / |