Patients included in current study (n = 57) | |
---|---|
Onset age, median (IQR), years | 6.42 (5.30) |
Male, n (%) | 28 (49.1%) |
Time to initiation of therapy, median (IQR), months | 1.00 (1.00) |
Follow-up period, median (IQR), months | 54.00 (75.00) |
Number of the affected joints, median (IQR) | 5 (11) |
Manifestations, n (%) | |
Fever | 57 (100%) |
Skin Rash | 50 (87.7%) |
Joint Swelling or arthralgia | 57 (100%) |
Hepatomegaly | 16 (28.1%) |
Splenomegaly | 24 (42.1%) |
Lymphopathy | 30 (52.6%) |
Serositis | 13 (22.8%) |
MAS | 6 (10.5%) |
Lab examinnationa | |
ESR (mm/h) | 78.77 (30.63) |
CRP (mg/L) | 130.00 (109.83) |
SF (ng/ml) | 1376.00(2670.00) |
WBC (×10^9/L) | 16.14 (11.91) |
PLT (×10^9/L) | 444 (194) |