Table 1 Patients demographics. Data presented as n (%) unless stated
PRP (n = 14) | SRP (n = 16) | AC (n = 14) | Controls (n = 15) | p | |
|---|---|---|---|---|---|
Mean age at assessment (range) | 12.2 (6.1–15.6) | 11.9 (3.6–16) | 14.2 (6–16.6) | 12.4 (8.5–15.8) | ns |
Gender | 10F, 4 M | 11F, 5 M | 7F, 7 M | 12 F, 3 M | ns |
Underlying diagnosis | – | – | – | ||
dSSc | 10 (62.5) | ||||
lSSc | 2 (12.5) | ||||
MCTD | 2 (12.5) | ||||
SLE | 1 (6.3) | ||||
Overlap (SSc/SLE) | 1 (6.3) | ||||
Antibody profile | |||||
ANA | 2 | 16 (100) | 1 (8.3) | ||
ACA | – | 6 (37.5) | – | ||
Topo-1 | – | 7 (43.8) | – | ||
U1-RNP | – | 6 (37.5) | – | ||
Capillaroscopy | |||||
Scleroderma pattern active | – | 8 (50) | – | ||
Scleroderma pattern late | – | 3 (18.8) | – | ||
Scleroderma pattern early | – | 1 (6.3) | – | ||
Non-specific | 7 (50) | 4 (25) | – | ||
Acrocyanosis pattern | – | – | 8 (57.1) | ||