From: 10th Congress of International Society of Systemic Auto-Inflammatory Diseases (ISSAID)
Outcome and status | Patient 1 | Patient 2 | Patient 3 |
---|---|---|---|
Alive, 6 yrs | Dead, 6 mos | Dead, 1.5yrs | |
Fever | + | + | + |
Skin rash | + | + | + |
Hepato-Splenomegaly | + | + | + |
Hemophagocytic lymphohistiocytosis | + | + | + |
Gastrointestinal symptoms | + | + | + |
Cytopenia | + | + | + |
Acute phase response | + | + | + |
Bone marrow dysplasia | + | + | + |